Neurofibromatosis (Von Recklinghausen's Diseased) in Mediastinum -3 case-

종격동에 발생한 다발성 신경섬유종증 -3례 보고-

  • Pyeon, Seung-Hwan (Dept.of Thoracic and Cardiovascular Surgery, College of Medicine, Dong-A University) ;
  • Jeong, Il-Yeong (Dept.of Thoracic and Cardiovascular Surgery, College of Medicine, Dong-A University) ;
  • Choe, Pil-Jo (Dept.of Thoracic and Cardiovascular Surgery, College of Medicine, Dong-A University) ;
  • U, Jong-Su (Dept.of Thoracic and Cardiovascular Surgery, College of Medicine, Dong-A University)
  • 편승환 (동아대학교 의과대학 흉부외 과학교실) ;
  • 정일영 (동아대학교 의과대학 흉부외 과학교실) ;
  • 최필조 (동아대학교 의과대학 흉부외 과학교실) ;
  • 우종수 (동아대학교 의과대학 흉부외 과학교실)
  • Published : 1996.01.01

Abstract

We report three cases of posterior mediastinal tumor in Von Recklinghausen's disease on 12-yearsy old boy, 8-years-old girl and 6-years-old boy. Especially the last case was combinded with "Dumbbell" neurilemmoma of cervical spine. In the first case, preoperative CT scan showed a homogeneous large mass In the posterior mediastinum. But the mass did not show intraspinal invasion on the chest MRI scan. In the last case, cervical spine CT with thecal enhancement shows dumbbell shaped neurofibroma, compressed spinal cord and thecal sac In three cases we removed all the masses successfully and the patients were discharged safely without significant problem.t problem.

Keywords

References

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