Syngnathia: Review of literature and a case report

선천성 악골유합증

  • Lee Jong-Ho (Department of Oral and Maxillofacial Surgery, College of Dentistry, Seoul National University) ;
  • Kim Yong-Hun (Department of Oral and Maxillofacial Surgery, College of Dentistry, Seoul National University) ;
  • Seo Byoung-Moo (Department of Oral and Maxillofacial Surgery, College of Dentistry, Seoul National University) ;
  • Choi Jin-Young (Department of Oral and Maxillofacial Surgery, College of Dentistry, Seoul National University) ;
  • Choung Pill-Hoon (Department of Oral and Maxillofacial Surgery, College of Dentistry, Seoul National University) ;
  • Kim Myung-Jin (Department of Oral and Maxillofacial Surgery, College of Dentistry, Seoul National University)
  • 이종호 (서울대학교 치과대학 구강악안면외과학교실) ;
  • 김용훈 (서울대학교 치과대학 구강악안면외과학교실) ;
  • 서병무 (서울대학교 치과대학 구강악안면외과학교실) ;
  • 최진영 (서울대학교 치과대학 구강악안면외과학교실) ;
  • 정필훈 (서울대학교 치과대학 구강악안면외과학교실) ;
  • 김명진 (서울대학교 치과대학 구강악안면외과학교실)
  • Published : 2001.06.01

Abstract

Congenital craniofacial disorders represent approximately 20% of all birth defects, One of these disorders is syngnathia, Congenital fusion of the maxilla and mandible is rare and can present in a wide range of severity from single mucosal band(synechiae) to complete bony fusion(syngnathia), Syngnathia, congenital bony fusion of the mandible and maxilla, is even less common than synechiae, with only 25 cases reported in the literature, Most of them have presented as an incomplete, unilateral fusion, We report a case of unilateral bony fusion of the maxilla, mandible, and zygomatic arch, Details of operative management and follow-up data are presented with review of literature.

악골유합증은 두경부의 매우 드문 선천적 기형으로, 상악과 하악간의 골성 유합이 그 특징이다. 저자들은 좌측 상악, 하악 및 관골궁의 골성 유합을 보이는 1 예를 경험하였고, 골성 유합의 분리를 위한 수술을 시행하였으며, 이후 장기 예후 관찰기간중 개구제한의 점차적인 재발을 관찰하였기에 이에 보고하는 바이다.

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