Alveolar Soft Part Sarcoma Metastatic to the Brain - A Case Report -

뇌로 전이된 포상 연부 육종 - 증례보고 -

  • Cheong, Jin Hwan (Department of Neurosurgery, Hanyang University Kuri Hospital) ;
  • Kim, Choong Hyun (Department of Neurosurgery, Hanyang University Kuri Hospital) ;
  • Bak, Koang Hum (Department of Neurosurgery, Hanyang University Kuri Hospital) ;
  • Kim, Jae Min (Department of Neurosurgery, Hanyang University Kuri Hospital) ;
  • Oh, Suck Jun (Department of Neurosurgery, Hanyang University Kuri Hospital)
  • 정진환 (한양대학교 의과대학 구리병원 신경외과학교실) ;
  • 김충현 (한양대학교 의과대학 구리병원 신경외과학교실) ;
  • 백광흠 (한양대학교 의과대학 구리병원 신경외과학교실) ;
  • 김재민 (한양대학교 의과대학 구리병원 신경외과학교실) ;
  • 오석전 (한양대학교 의과대학 구리병원 신경외과학교실)
  • Received : 2000.11.30
  • Accepted : 2001.07.02
  • Published : 2001.06.28

Abstract

Alveolar Soft Part Sarcoma(ASPS) is a rare entity that invariably ends in death from the disseminated disease. Although the most common site of metastasis is the lung, the central nervous system is also the third common site. Its histogenesis remains to be unknown and the gold standard treatment is radically surgical removal of the mass. However, adjuvant chemotherapy and radiotherapy are known to be less effective. The authors present a 24-year-old man who was admitted with headache and neck discomfort. Magnetic resonance( MR) imaging scans demonstrated multiple masses in the left frontal lobe, parietal lobe, and right cerebellum. The patient underwent surgery to remove multiple masses in the staged fashion. The postoperative course was uneventful, but the patient committed suicide 5 months later. The authors reviewed the pertinent literature and discussed this clinical entity with references.

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