Tuberculosis and Respiratory Diseases

  • 제50권1호
  • /
  • Pages.122-126
  • /
  • 2001
  • /
  • 1738-3536(pISSN)
  • /
  • 2005-6184(eISSN)
대한결핵및호흡기학회 (The Korean Academy of Tuberculosis and Respiratory Diseases)
권호 표지

신경섬유종증에 동반된 가성동맥류 파열로 발생한 자연 혈흉 1예

A Case of Spontaneous Hemothorax Due to Rupture of Pseudoaneurysm in Type 1 Neurofibromatosis

  • 김순종 (울산대학교 의과대학 서울중앙병원 내과학교실) ;
  • 정훈 (울산대학교 의과대학 서울중앙병원 내과학교실) ;
  • 이성순 (울산대학교 의과대학 서울중앙병원 내과학교실) ;
  • 임채만 (울산대학교 의과대학 서울중앙병원 내과학교실) ;
  • 이상도 (울산대학교 의과대학 서울중앙병원 내과학교실) ;
  • 고윤석 (울산대학교 의과대학 서울중앙병원 내과학교실) ;
  • 김우성 (울산대학교 의과대학 서울중앙병원 내과학교실) ;
  • 김동순 (울산대학교 의과대학 서울중앙병원 내과학교실) ;
  • 김원동 (울산대학교 의과대학 서울중앙병원 내과학교실) ;
  • 심태선 (울산대학교 의과대학 서울중앙병원 내과학교실)
  • Kim, Sun-Jong (Department of Internal Medicine, University of Ulsan, College of Medicine, Asan Medical Center) ;
  • Jeong, Hoon (Department of Internal Medicine, University of Ulsan, College of Medicine, Asan Medical Center) ;
  • Lee, Sung-Soon (Department of Internal Medicine, University of Ulsan, College of Medicine, Asan Medical Center) ;
  • Lim, Chae-Man (Department of Internal Medicine, University of Ulsan, College of Medicine, Asan Medical Center) ;
  • Lee, Sang-Do (Department of Internal Medicine, University of Ulsan, College of Medicine, Asan Medical Center) ;
  • Koh, Youn-Suck (Department of Internal Medicine, University of Ulsan, College of Medicine, Asan Medical Center) ;
  • Kim, Woo-Sung (Department of Internal Medicine, University of Ulsan, College of Medicine, Asan Medical Center) ;
  • Kim, Dong-Soon (Department of Internal Medicine, University of Ulsan, College of Medicine, Asan Medical Center) ;
  • Kim, Won-Dong (Department of Internal Medicine, University of Ulsan, College of Medicine, Asan Medical Center) ;
  • Shim, Tae-Sun (Department of Internal Medicine, University of Ulsan, College of Medicine, Asan Medical Center)
  • 발행 : 2001.01.30
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초록

저자들은 신경섬유종증 환자에서 우측 내유동맥에 생긴 가성동맥류의 파열로 인한 자연 혈흉을 진단하고 혈관색전술로 치료한 1예를 경험하였기에 문헌 고찰과 함께 보고하는 바이다.

A non-traumatic, spontaneous hemothorax is rare. The most common causes are coagulopathy, due to anticoagulation treatment, and cancers with a metastasis to the pleural surface. Other unusual causes include thoracic endometriosis, ruptured aortic aneurysm, pulmonary arterio-venous malformation, coagulopathy, Osler-Rendeu-Weber syndrome, Ehlers-Danlos syndrome et cetera. A type 1 neurofibromatosis(Von Recklinghausen's disease) is an autosomal dominant disease that is characterized by multiple skin tumors(neurofibroma) and abnormal skin pigmentation(caf$\acute{e}$-au-lait spots). Some are accompanied by vasculopathy, and are present with a spontaneous hemothorax. Such cases are unusual but fatal. We have recently experienced a case where a young male patient with neurofibromatosis initially presented with hypovolemic shock due to a spontaneous hemothorax. Later, aortography revealed that the cause of the hemothorax was a rupture of a pseudoaneurysm of the right internal mammary artery and as a result, an embolization was performed. Here we report this case with a review of the appropriate literature.

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