Pediatric Gastroenterology, Hepatology & Nutrition

The Korean Society of Pediatric Gastroenterology, Hepatology and Nutrition (대한소아소화기영양학회)
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A Case of Cholangiocarcinoma Arising from Type I Choledochal Cyst in a 13-year-old Girl

13세 여아에서 발생한 총담관낭 I형에서 기원한 담관암 1례

  • Ahn, Sung-Ryon (Department of Pediatrics, College of Medicine, Pusan National University) ;
  • Nam, Sang-Ook (Department of Pediatrics, College of Medicine, Pusan National University) ;
  • Park, Jae-Hong (Department of Pediatrics, College of Medicine, Pusan National University) ;
  • Lim, Young-Tak (Department of Pediatrics, College of Medicine, Pusan National University) ;
  • Lee, Jun-Woo (Department of Radiology, College of Medicine, Pusan National University) ;
  • Lee, Chang-Hun (Department of Pathology, College of Medicine, Pusan National University)
  • 안성연 (부산대학교 의과대학 소아과학교실) ;
  • 남상욱 (부산대학교 의과대학 소아과학교실) ;
  • 박재홍 (부산대학교 의과대학 소아과학교실) ;
  • 임영탁 (부산대학교 의과대학 소아과학교실) ;
  • 이준우 (부산대학교 의과대학 진단방사선과학교실) ;
  • 이창훈 (부산대학교 의과대학 병리학교실)
  • Received : 2002.03.07
  • Accepted : 2002.03.20
  • Published : 2002.03.30
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Abstract

Choledochal cyst is a rare developmental malformation of the biliary tree and has serious problem of transformation to malignancy. The development of cholangiocarcinoma related to choledochal cyst increases as the age of patient increases and is more common in Orientals with female predominance of 2.5 times. Prevalence rate of cholangiocarcinoma is various from 2.5 to 15.6% in adult with choledochal cyst, but very low in children. We experienced a case of cholangiocarcinoma with multiple liver metastases arising from type I choledochal cyst in a 13-year-old girl who complained of sudden onset of right upper quadrant abdominal pain.

저자들은 갑작스럽게 발생한 우상복부 동통을 주소로 내원한 13세 여아에서 간에 다발성으로 전이가 된 I형 총담관낭으로부터 발생한 담관암 1례를 경험하였기에 보고하는 바이다.

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