Two Cases of Microscopic Polyangiitis with Honeycomb Lung

봉소상 폐(Honeycomb Lung) 소견을 보인 현미경적 다발성 혈관염 2예

  • Hahn, Hye-Sook (Department of Internal Medicine, Gachon Medical School, Gil Medical Center) ;
  • Hwang, Jun-Kyu (Department of Internal Medicine, Gachon Medical School, Gil Medical Center) ;
  • Jung, Hyuk-Sang (Department of Internal Medicine, Gachon Medical School, Gil Medical Center) ;
  • Song, Suk-Ho (Department of Internal Medicine, Gachon Medical School, Gil Medical Center) ;
  • Joo, Kwon-Wook (Department of Internal Medicine, Gachon Medical School, Gil Medical Center) ;
  • Park, Gye-Young (Department of Internal Medicine, Gachon Medical School, Gil Medical Center) ;
  • Lee, Jong-Ho (Department of Internal Medicine, Gachon Medical School, Gil Medical Center) ;
  • Oh, Young-Ha (Department of Internal Pathology, Gachon Medical School, Gil Medical Center) ;
  • Lee, Hyoun-Joo (Department of Internal Radiology, Gachon Medical School, Gil Medical Center)
  • 한혜숙 (가천의대 중앙길병원 내과) ;
  • 황준규 (가천의대 중앙길병원 내과) ;
  • 정혁상 (가천의대 중앙길병원 내과) ;
  • 송석호 (가천의대 중앙길병원 내과) ;
  • 주권욱 (가천의대 중앙길병원 내과) ;
  • 박계영 (가천의대 중앙길병원 내과) ;
  • 이종호 (가천의대 중앙길병원 내과) ;
  • 오영하 (가천의대 중앙길병원 해부병리과) ;
  • 이현주 (가천의대 중앙길병원 진단방사선과)
  • Published : 2002.05.30

Abstract

Microscopic polyangiitis is a systemic small-vessel vasculitis that is associated primarily with necrotizing glomerulonephritis and pulmonary capillaritis. A recurrent and diffuse alveolar hemorrhage due to pulmonary capillaritis is the main clinical manifestation of lung involvement. Recently, and interstitial lung disease that mimics idiopathic pulmonary fibrosis was reported to be rarely associated with microscopic polyangiitis. Here we report two patients with microscopic polyangiitis who showed a honeycomb lung at the time of the initial diagnosis with a brief review of relevant literature.

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