Pediatric Gastroenterology, Hepatology & Nutrition
- Volume 6 Issue 2
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- Pages.215-220
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- 2003
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- 2234-8646(pISSN)
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- 2234-8840(eISSN)
A Case of Diencephalic Syndrome Presented as Failure to Thrive from Three Month of Age
생후 3개월부터 성장장애를 보이기 시작한 간뇌 증후군(Diencephalic Syndrome) 1례
- Kim, Seung-Soo (Department of Pediatrics, Sunchunhyang University Hospital) ;
- Kim, Sung-Shin (Department of Pediatrics, Sunchunhyang University Hospital) ;
- Park, Jae-Ock (Department of Pediatrics, Sunchunhyang University Hospital) ;
- Kim, Chang-Whi (Department of Pediatrics, Sunchunhyang University Hospital)
- 김승수 (순천향대학교 의과대학 소아과학교실) ;
- 김성신 (순천향대학교 의과대학 소아과학교실) ;
- 박재옥 (순천향대학교 의과대학 소아과학교실) ;
- 김창휘 (순천향대학교 의과대학 소아과학교실)
- Received : 2003.09.02
- Accepted : 2003.09.13
- Published : 2003.09.30
Abstract
A 14-month-old child visited emergency room with stuporous mental state. He had been suffering from failure to thrive (FTT) and emaciation since three months of age, but he had good appetite and had been euphoric. A large mass was found in the third ventricle by brain CT and MRI. His parents refused operative removal of the mass and he expired 14 days after admission. It is necessary to include diencephalic syndrome in the differential diagnosis of failure to thrive when infants show FTT despite of good appetite and euphoric status.
저자들은 생후 3개월부터 심한 성장장애를 보였던 남아가 14개월에 두 개 내 종양에 의해 발생한 간뇌증후군으로 진단되었기에 보고하는 바이다. 소아에서 적당한 양을 섭취하고 식욕이 유지됨에도 불구하고 현저한 성장장애와 체중 증가 부진을 보이는 경우에는 간뇌증후군의 감별이 필요할 것으로 사료된다.