Annals of Clinical Neurophysiology

The Korean Society of Clinical Neurophysiology (대한임상신경생리학회)
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A Case of Polyneuropathy of the POEMS Syndrome Responsive to Intravenous Immunoglobulin

Immunoglobulin으로 호전된 POEMS 증후군의 다발성 신경병증 1예

  • Bae, Sang-Woo (Department of Neurology, Dankook University Hospital) ;
  • Kwon, Jun-Woo (Department of Neurology, Dankook University Hospital) ;
  • Yoon, Sook (Department of Neurology, Dankook University Hospital) ;
  • Chang, Yoon-Jeong (Department of Neurology, Dankook University Hospital) ;
  • Lee, Chang-Min (Department of Neurology, Dankook University Hospital) ;
  • Lee, Geun-Ho (Department of Neurology, Dankook University Hospital) ;
  • Kim, Jae-Il (Department of Neurology, Dankook University Hospital)
  • 배상우 (단국대학교 의과대학 신경과학교실) ;
  • 권준우 (단국대학교 의과대학 신경과학교실) ;
  • 윤숙 (단국대학교 의과대학 신경과학교실) ;
  • 장윤정 (단국대학교 의과대학 신경과학교실) ;
  • 이창민 (단국대학교 의과대학 신경과학교실) ;
  • 이근호 (단국대학교 의과대학 신경과학교실) ;
  • 김재일 (단국대학교 의과대학 신경과학교실)
  • Published : 2003.12.30
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Abstract

POEMS syndrome is a multisystem disorder associated with polyneuropathy, organomegaly, endocrinopathy, a monoclonal protein(M-protein), and skin change. Recently we have had the opportunity to attend one patient with clinical features similar to this syndrome. He was a 46-year-old man who had a progressive polyneuropathy, swallowing difficulty, hepatosplenomegaly, hypothyroidism, IgA ${\lambda}type$ monoclonal gammapathy, specific skin change and ascites. His symptoms such as low extrimity pain and weakness, swallowing difficulty were improved by high-dose 7S-IgG. Thus, we report a case with a review of the literature.

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