Korean Journal of Bronchoesophagology (대한기관식도과학회지)

The Korean Bronchoesophagological Society (대한기관식도과학회)
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A Case of an EXIT procedure for Airway management of fetus with Agnathia

하악결손증 태아에서 기도확보를 위해 시행한 EXIT 시술 1례

  • Bong Jeong Pyo (Department of Otorhinolaryngology-Head and Neck Surgery Wonju College of Medicine, Yonsei University) ;
  • Kim Yoo Jung (Department of Otorhinolaryngology-Head and Neck Surgery Wonju College of Medicine, Yonsei University) ;
  • Yang Jong Won (Department of Otorhinolaryngology-Head and Neck Surgery Wonju College of Medicine, Yonsei University) ;
  • Kim Jin Hyung (Department of Otorhinolaryngology-Head and Neck Surgery Wonju College of Medicine, Yonsei University) ;
  • Kim Tae Hwan (Department of Otorhinolaryngology-Head and Neck Surgery Wonju College of Medicine, Yonsei University) ;
  • Choi Seong Jin (Department of Obsterics and Gynecology, Wonju College of Medicine Yonsei University)
  • 봉정표 (연세대학교 원주의과대학 이비인후-두경부외과학교실) ;
  • 김유정 (연세대학교 원주의과대학 이비인후-두경부외과학교실) ;
  • 양종원 (연세대학교 원주의과대학 이비인후-두경부외과학교실) ;
  • 김진형 (연세대학교 원주의과대학 이비인후-두경부외과학교실) ;
  • 김태환 (연세대학교 원주의과대학 이비인후-두경부외과학교실) ;
  • 최성진 (연세대학교 원주의과대학 이비인후-산부인과학교실)
  • Published : 2005.06.01
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Abstract

This study aimed to report a case of infant who presented with a prenatal ultrasound diagnosis of agnathia, polyhydramnios followed by a review of previous studies. As widely acknowledge, agnathia is a complex lethal malformation characterized by absent mandible, microstomia, microglossia and ear anomaly which are secondary results to a defect of the first branchial auh. Newborn infants with agnathia often suffer from airway obstruction, causing fatal respiratory failure. The most difficult part of treating those newborns is to keep the airway patent. Therefore, as early airway management planning as possible is the most important part. Airway management was achieved with tracheotomy through an ex utero intrapartum treatment procedure(EXIT). The case of this infant, reporting here, was underwent tracheotomy with preservation of uteroplacental blood flow and gas exchange.

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