Maxillofacial Plastic and Reconstructive Surgery

Korean Association of Maxillofacial Plastic and Reconstructive Surgeons (대한악안면성형재건외과학회)
권호 표지

TREATMENT OF A PATIENT WITH CLEIDOCRANIAL DYSPLASIA USING IMPLANT-SUPPORTED BAR OVERDENTURE: A CASE REPORT

바 피개의치를 이용한 쇄골두개이형성증 환자의 치료: 증례보고

  • Jang, Jung-Hui (Dept. of Oral and Maxillofacial Surgery, Gil Medical Center, Gachon Medical School) ;
  • Song, Min-Seok (Dept. of Oral and Maxillofacial Surgery, Gil Medical Center, Gachon Medical School) ;
  • Kim, Hyeon-Min (Dept. of Oral and Maxillofacial Surgery, Gil Medical Center, Gachon Medical School) ;
  • Kim, Nam-Hun (Dept. of Oral and Maxillofacial Surgery, Gil Medical Center, Gachon Medical School) ;
  • Eom, Min-Yong (Dept. of Oral and Maxillofacial Surgery, Gil Medical Center, Gachon Medical School) ;
  • Koo, Hyun-Mo (Dept. of Oral and Maxillofacial Surgery, Gil Medical Center, Gachon Medical School) ;
  • Yi, Jun-Kyu (Dept. of Oral and Maxillofacial Surgery, Gil Medical Center, Gachon Medical School) ;
  • Jeong, Jong-Cheol (Sam More Dental Clinic) ;
  • Kim, Se-Woong (Dept. of Prosthodontics, Gil Medical Center, Gachon Medical School)
  • 장중희 (가천의과대학교 길병원 구강악안면외과) ;
  • 송민석 (가천의과대학교 길병원 구강악안면외과) ;
  • 김현민 (가천의과대학교 길병원 구강악안면외과) ;
  • 김남훈 (가천의과대학교 길병원 구강악안면외과) ;
  • 엄민용 (가천의과대학교 길병원 구강악안면외과) ;
  • 구현모 (가천의과대학교 길병원 구강악안면외과) ;
  • 이준규 (가천의과대학교 길병원 구강악안면외과) ;
  • 정종철 (샘 모아치과) ;
  • 김세웅 (가천의과대학교 길병원 보철과)
  • Published : 2006.01.31
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Abstract

Cleidocranial dysplasia is rare inherited skeletal dysplasia. It was first reported by Martin in 1765. Subsequently, Marie and Sainton independently documented the criteria of the disease. Cleidocranial dysplasia is a bone disorder caused by a defect in the CBFA1 gene of chromosome 6p21. This gene guides osteoblastic differentiation and appropriate bone formation. Patient with cleidocranial dysplasia has maxillary deficiency, high and narrow palate, prolonged retention of primary teeth, unerupted permanent teeth and supernumerary teeth. Therapeutic options in these patients include of autotransplantation of selected impacted teeth, forced eruption of permanent teeth, full denture, overdenture and implant-supported prosthesis. We report a patient with cleidocranial dysplasia. This patient was treated with implant supported bar overdenture. Despite of gene defect that affects osteoblastic activity, bone remodeling and osseointegration occurred in our patient. So, we report this case with review of literature.

Keywords

References

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