Archives of Plastic Surgery

Korean Society of Plastic and Reconstructive Surgeons (대한성형외과학회)
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Malignant Peripheral Nerve Sheath Tumor of Scalp

두피에 발생한 악성말초신경초종양

  • Lee, Ki Young (Departments of Plastic Surgery, College of Medicine, The Catholic University of Korea) ;
  • Bae, Joon Sung (Departments of Plastic Surgery, College of Medicine, The Catholic University of Korea) ;
  • Jun, Young Joon (Departments of Plastic Surgery, College of Medicine, The Catholic University of Korea) ;
  • Lee, Hee Jeong (Departments of Pathology, College of Medicine, The Catholic University of Korea) ;
  • Kim, Young Jin (Departments of Plastic Surgery, College of Medicine, The Catholic University of Korea)
  • 이기영 (가톨릭대학교 의과대학 성형외과학교실) ;
  • 배준성 (가톨릭대학교 의과대학 성형외과학교실) ;
  • 전영준 (가톨릭대학교 의과대학 성형외과학교실) ;
  • 이희정 (가톨릭대학교 의과대학 병리학교실) ;
  • 김영진 (가톨릭대학교 의과대학 성형외과학교실)
  • Received : 2007.04.19
  • Published : 2007.07.10
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Abstract

Purpose: Malignant peripheral nerve sheath tumors (MPNSTs) are rare neoplasms, usually arising from somatic soft tissues or peripheral nerves. Primary MPNST of the scalp is extremely rare. The case is being reported for its rarity. Methods: A 53-year-old female was presented with a scalp mass on vertex area. The tumor was localized in scalp skin and did not invade underlying periosteum or skull and treated with complete surgical excision followed by adjuvant chemotherapy and radiotherapy. Results: Histologically, the tumor showed malignant spindle cells with focal S-100 positivity on immunohistochemistry and a diagnosis of MPNST was made. Conclusion: Authors experienced a rare case of primary scalp MPNST and report the case.

Keywords

References

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