구개열과 동반된 선천성 구개 기형종 1례

A Case of Congenital Palatal Teratoma Associated with Cleft Palate

  • 송현석 (아주대학교 의과대학 성형외과학교실) ;
  • 박동하 (아주대학교 의과대학 성형외과학교실) ;
  • 배남석 (아주대학교 의과대학 성형외과학교실) ;
  • 박명철 (아주대학교 의과대학 성형외과학교실)
  • Song, Hyun Suk (Department of Plastic and Reconstructive Surgery, School of Medicine, Ajou University) ;
  • Park, Dong Ha (Department of Plastic and Reconstructive Surgery, School of Medicine, Ajou University) ;
  • Pae, Nam Suk (Department of Plastic and Reconstructive Surgery, School of Medicine, Ajou University) ;
  • Park, Myong Chul (Department of Plastic and Reconstructive Surgery, School of Medicine, Ajou University)
  • 투고 : 2007.03.26
  • 발행 : 2007.07.10

초록

Purpose: The oral teratoma is found approximately in live birth at the rate from 1 : 35,000 to 1 : 200,000. In a review of literature 16 cases of midline teratoma with cleft palate were reported. We report a case of congenital palatal teratoma with cleft palate in a 1-year-old girl. Methods: A 1-year-old girl was admitted our institution for the closure of cleft palate. On the intraoperative findings there was $4{\times}1{\times}0.5cm$ sized hairy soft mass at the midline and complete cleft palate. We did incisional biopsy intraoperatively and its pathology revealed heterotopic brain tissue. The excision of remaining mass and palatoplasty with Sommerlad's method were performed. The final pathology of the mass was mature cystic teratoma. Results: After the operation there were neither recurrence nor oronasal regurgitation. Conclusion: We report for one patient with congenital palatal teratoma associated with cleft palate and obtained an excellent result.

키워드

참고문헌

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