Tuberculosis and Respiratory Diseases

The Korean Academy of Tuberculosis and Respiratory Diseases (대한결핵및호흡기학회)
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A Case of Lymphangioleiomyomatosis Combined with Chylothorax and Bilateral Pneumothoraces

유미흉과 양측성 기흉을 동반한 폐 림프관평활근종증 1예

  • Kim, Jong-Hwa (Division of Respiratory & Allergy Medicine, Department of Internal Medicine, Soonchunhyang University, School of Medicine) ;
  • Kim, Yang-Ki (Division of Respiratory & Allergy Medicine, Department of Internal Medicine, Soonchunhyang University, School of Medicine) ;
  • Kim, Jung-Hyun (Division of Respiratory & Allergy Medicine, Department of Internal Medicine, Soonchunhyang University, School of Medicine) ;
  • Lee, Young Mok (Division of Respiratory & Allergy Medicine, Department of Internal Medicine, Soonchunhyang University, School of Medicine) ;
  • Kim, Ki-Up (Division of Respiratory & Allergy Medicine, Department of Internal Medicine, Soonchunhyang University, School of Medicine) ;
  • Uh, Soo-taek (Division of Respiratory & Allergy Medicine, Department of Internal Medicine, Soonchunhyang University, School of Medicine) ;
  • Noh, Hyung-Jun (Department of Radiology, Soonchunhyang University, School of Medicine) ;
  • Kim, Hyun Jo (Department of Chest Surgery, Soonchunhyang University, School of Medicine) ;
  • Jang, Won Ho (Department of Chest Surgery, Soonchunhyang University, School of Medicine) ;
  • Kim, Dong-Won (Department of Clinical Pathology, Soonchunhyang University, School of Medicine)
  • 김종화 (순천향대학교 내과학교실) ;
  • 김양기 (순천향대학교 내과학교실) ;
  • 김정현 (순천향대학교 내과학교실) ;
  • 이영목 (순천향대학교 내과학교실) ;
  • 김기업 (순천향대학교 내과학교실) ;
  • 어수택 (순천향대학교 내과학교실) ;
  • 노형준 (순천향대학교 진단방사선과교실) ;
  • 김현조 (순천향대학교 흉부외과학교실) ;
  • 장원호 (순천향대학교 흉부외과학교실) ;
  • 김동원 (순천향대학교 임상병리학교실)
  • Received : 2006.12.28
  • Accepted : 2007.05.28
  • Published : 2007.06.30
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Abstract

A 29-year-old female patient presented with exertional dyspnea that she had suffered with for 2 months. The chest X-ray displayed right pleural effusion that was diagnosed as chyle, according to the level of cholesterol and triglyceride in the pleural fluid. VATS (video assisted thoracic surgery) of the right lung was performed on the 7th day of hospitalization for obtaining a lung biopsy and to control the of pneumochylothorax. On the 11th hospitalization day, VATS of left lung was also performed to control the recurrent pneumothorax via pleurodesis. The lung biopsy showed moderate amounts of spindle-shaped and rounded cells (so-called LAM cells), which were reactive to actin and HMB45 (on immunohistochemical stains). We report here on a rare case of lymphangioleiomyomatosis combined with chylothorax and bilateral pneumothroraces.

본 저자들은 국내외적으로 그 발생이 드문 양측성 기흉과 유미흉을 동반한 LAM 1예를 경험하였기에 문헌고찰과 함께 보고하는 바이다.

Keywords

References

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