Pediatric Gastroenterology, Hepatology & Nutrition

The Korean Society of Pediatric Gastroenterology, Hepatology and Nutrition (대한소아소화기영양학회)
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Calcifying Fibrous Tumor Mimicking a Foreign Body of the Stomach: A Case Report

위 내 이물로 오인한 석회화 섬유 종양 1예

  • Jeong, Ji-Eun (Department of Pediatrics, School of Medicine, Catholic University of Daegu) ;
  • Lee, Kyung-Hun (Department of Pediatrics, School of Medicine, Catholic University of Daegu) ;
  • Sung, Hyun-Jung (Department of Pathology, School of Medicine, Catholic University of Daegu) ;
  • Cho, Chang-Ho (Department of Pathology, School of Medicine, Catholic University of Daegu)
  • 정지은 (대구가톨릭대학교 의과대학 소아과학교실) ;
  • 이경훈 (대구가톨릭대학교 의과대학 소아과학교실) ;
  • 성현정 (대구가톨릭대학교 의과대학 병리과학교실) ;
  • 조창호 (대구가톨릭대학교 의과대학 병리과학교실)
  • Received : 2009.02.03
  • Accepted : 2009.02.27
  • Published : 2009.03.30
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Abstract

Calcifying fibrous tumors (CFTs) are unusual benign tumors of childhood, located primarily in soft tissues, pleura, and peritoneum. The cause and pathogenesis are unclear. We report a rare case of a CFT in a 2-year-old boy who presented with vomiting and abdominal distension. An abdominal X-ray showed an elliptical, calcific shadow in the LUQ area mimicking a foreign body. An internally protruding mass along the lesser curvature of the gastric body was an incidental finding during upper endoscopy, biopsies of which were negative. Abdominal CT showed a 4.5${\times}$3.2 cm soft tissue mass of the gastric wall with calcifications. A diagnosis of gastric submucosal mass was suspected and a wedge resection of the stomach was performed. On microscopic examination, the tumor was composed of whorls of dense hyalinized collagen bundles with a few fibroblasts. There were also amorphous dystrophic calcifications and nodular aggregates of mononuclear inflammatory cells. Immunohistochemically, spindle cells did not stain for anaplastic lymphoma kinase-1 (ALK-1), CK, smooth muscle actin (SMA), or desmin. Taken together, the mass was compatible with a CFT of the gastric wall. This is the first reported case of CFT in a Korean child.

평소 복부 팽만을 보인 2세 남아가 내원 3일 전부터 간헐적인 구토를 동반하여 시행한 복부 방사선 사진에서 좌상복부에서 석회화 소견을 관찰하여 상부 위장관내시경과 복부 전산화 단층 사진을 시행하였다. 술 후 병리 검사에서 상당히 빈도가 드문 석회화 섬유 종양을 발견하였기에 보고하는 바이다.

Keywords

References

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