Investigative Magnetic Resonance Imaging

Korean Society of Magnetic Resonance in Medicine (대한자기공명의과학회)
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Ancient Schwannoma of the Thigh mimicking a Plexiform Malignant Peripheral Nerve Sheath Tumor: A Case Report

총상악성말초신경초종양으로 오인한 넓적다리에 생긴 고대 신경초종: 1예 보고

  • Lee, Yeon-Soo (Department of Radiology, Daejeon St. Mary's Hospital, The Catholic University of Korea) ;
  • Park, Sang-Eun (Department of Orthopedic Surgery, Daejeon St. Mary's Hospital, The Catholic University of Korea) ;
  • Lee, Jung-Uee (Department of Pathology, Daejeon St. Mary's Hospital, The Catholic University of Korea)
  • 이연수 (가톨릭대학교 의과대학 대전성모병원 영상의학과) ;
  • 박상은 (가톨릭대학교 의과대학 대전성모병원 정형외과) ;
  • 이정의 (가톨릭대학교 의과대학 대전성모병원 해부병리과)
  • Received : 2011.05.30
  • Accepted : 2011.07.28
  • Published : 2011.08.31
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Abstract

Ancient schwannoma is a rare variant of schwannoma and a slow growing benign tumor associated with degeneration that may be diagnosed as a malignant tumor, because it presents with a large size and an inhomogeneous signal intensity. The main differential diagnosis of plexiform soft tissue tumor includes plexiform neurofibroma, malignant peripheral nerve sheath tumor (MPNST). In this case, we describe the MRI findings in a case of ancient schwannoma involving left thigh of a 63-year-old woman mimicking a plexiform MPNST. The tumor appeared as an inhomogeneous signal intensity and multinodular appearance, causing misdiagnosis as a plexiform MPNST.

고대신경초종(ancient schwannoma)은 신경초종의 변이(variant)로서 천천히 자라나고 퇴행성 변화를 동반한 드문 양성종양으로 알려져 있으며 자기공명영상상 큰 크기와 불균질한 신호강도 때문에 악성 종양으로 오인될 수 있다. 연부조직 종양이 얼기모양(plexiform)을 보일때, 총상신경섬유종, 또는 악성말초신경초종양 등을 감별해야 한다. 이에 저자들은 63세 여자 환자의 왼쪽 넓적다리에 발생한 고대신경초종 1예를 경험하였기에 자기공명영상 소견을 보고하고자 한다. 자기공명영상에서 불균질한 신호강도와 다결절 소견을 보여 총상(plexiform) 악성 말초신경초종양으로 오인하였다.

Keywords

References

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