Journal of Chest Surgery

  • 제48권1호
  • /
  • Pages.90-94
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  • 2015
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  • 2765-1606(pISSN)
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  • 2765-1614(eISSN)
대한심장혈관흉부외과학회 (The Korean Society for Thoracic and Cardiovascular Surgery)
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A Successfully Treated Case of Gorham-Stout Syndrome with Sternal Involvement

  • Kim, Bong Jun (Department of Thoracic and Cardiovascular Surgery, Gangnam Severance Hospital, Yonsei University College of Medicine) ;
  • Kim, Tae Hoon (Department of Thoracic and Cardiovascular Surgery, Gangnam Severance Hospital, Yonsei University College of Medicine) ;
  • Kim, Do Jung (Department of Thoracic and Cardiovascular Surgery, Gangnam Severance Hospital, Yonsei University College of Medicine) ;
  • Noh, Dongsub (Department of Thoracic and Cardiovascular Surgery, Gangnam Severance Hospital, Yonsei University College of Medicine) ;
  • Haam, Seok Jin (Department of Thoracic and Cardiovascular Surgery, Gangnam Severance Hospital, Yonsei University College of Medicine) ;
  • Lee, Sungsoo (Department of Thoracic and Cardiovascular Surgery, Gangnam Severance Hospital, Yonsei University College of Medicine)
  • 투고 : 2014.04.28
  • 심사 : 2014.10.27
  • 발행 : 2015.02.05
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초록

Gorham-Stout Syndrome (GSS) is a rare disease characterized by localized bone resorption. Any part of the skeleton may be affected; therefore, symptoms can vary depending on the site involved. Pathological analysis reveals lymphovascular proliferation and osteolysis in the affected lesion, but the etiology of the disease is poorly understood. When GSS occurs in the chest, chylothorax or respiratory failure may occur. Thus far, a standard treatment for GSS has not been established, and the prognosis remains unknown. The following case report describes a successfully treated case of GSS in a 16-year-old boy with an affected sternum and ribs.

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참고문헌

  1. Gondivkar SM, Gadbail AR. Gorham-Stout syndrome: a rare clinical entity and review of literature. Oral Surg Oral Med Oral Pathol Oral Radiol Endod 2010;109:e41-8. https://doi.org/10.1016/j.tripleo.2009.08.043
  2. Chong Ng L, Sell P. Gorham disease of the cervical spine-a case report and review of the literature. Spine (Phila Pa 1976) 2003;28:E355-8. https://doi.org/10.1097/01.BRS.0000084557.38858.85
  3. Ruggieri P, Montalti M, Angelini A, Alberghini M, Mercuri M. Gorham-Stout disease: the experience of the Rizzoli Institute and review of the literature. Skeletal Radiol 2011; 40:1391-7. https://doi.org/10.1007/s00256-010-1051-9
  4. Heffez L, Doku HC, Carter BL, Feeney JE. Perspectives on massive osteolysis: report of a case and review of the literature. Oral Surg Oral Med Oral Pathol 1983;55:331-43. https://doi.org/10.1016/0030-4220(83)90185-8
  5. Brodszki N, Lansberg JK, Dictor M, et al. A novel treatment approach for paediatric Gorham-Stout syndrome with chylothorax. Acta Paediatr 2011;100:1448-53. https://doi.org/10.1111/j.1651-2227.2011.02361.x

피인용 문헌

  1. Chemical Pleurodesis Using Viscum album Extract in Gorham’s Disease Complicated with Chylothorax vol.33, pp.2, 2015, https://doi.org/10.4266/acc.2016.00164
  2. A rare case of Gorham-stout syndrome involving the thoracic spine with progressive bilateral chylothorax: a case report vol.20, pp.None, 2015, https://doi.org/10.1186/s12891-019-2542-z
  3. A Case of Vanishing Bones vol.41, pp.11, 2015, https://doi.org/10.1542/pir.2018-0297
  4. Gorham-Stout Disease in a Middle-Aged Patient Treated by Posterior Lateral Fusion: A Case Report and Literature Review vol.7, pp.2, 2021, https://doi.org/10.21129/nerve.2021.7.2.106