Journal of Oral Medicine and Pain

  • 제44권3호
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  • Pages.118-122
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  • 2019
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  • 2288-9272(pISSN)
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  • 2383-8493(eISSN)
대한안면통증구강내과학회 (Korean Academy of Orofacial Pain and Oral Medicine)
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Oral Manifestation of Paraneoplastic Pemphigus

  • Kim, Seurin (Department of Orofacial Pain and Oral Medicine, Dental Hospital of Yonsei University College of Dentistry) ;
  • Park, In Hee (Department of Orofacial Pain and Oral Medicine, Dental Hospital of Yonsei University College of Dentistry) ;
  • Park, YounJung (Department of Orofacial Pain and Oral Medicine, Dental Hospital of Yonsei University College of Dentistry) ;
  • Kwon, Jeong-Seung (Department of Orofacial Pain and Oral Medicine, Dental Hospital of Yonsei University College of Dentistry) ;
  • Choi, Jong-hoon (Department of Orofacial Pain and Oral Medicine, Dental Hospital of Yonsei University College of Dentistry) ;
  • Ahn, Hyung-Joon (Department of Orofacial Pain and Oral Medicine, Dental Hospital of Yonsei University College of Dentistry)
  • 투고 : 2019.06.14
  • 심사 : 2019.07.09
  • 발행 : 2019.09.30
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초록

Paraneoplastic pemphigus (PNP) is a rare and often fatal autoimmune blistering disease accompanied by both benign and malignant neoplasms. Usually, oral, skin, and mucosal lesions are the earliest manifestations shown by PNP patients. Oral ulcers are initial lesions in various autoimmune diseases like pemphigus, bullous pemphigoid, erythema multiforme, graft-versus-host, lichen planus, it does not improved despite of high-dose steroid therapy. We report a-35-year-old female who presented oral ulceration, lip crust and skin lesions. By doing several examinations, such as enzyme-linked immunosorbent assay, incisional biopsy with indirect immunofluorescence, she was diagnosed PNP with non-Hodgkin's lymphoma on pancreas.

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참고문헌

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