대한치과의사협회지 (The Journal of the Korean dental association)

  • 제57권2호
  • /
  • Pages.93-99
  • /
  • 2019
  • /
  • 0376-4672(pISSN)
  • /
  • 2713-7961(eISSN)
대한치과의사협회 (The Korean Dental Association)
권호 표지

구개열을동반한저한성외배엽형성이상환자의 악교정수술을포함한치료: A Clinical report

Treatment including orthognathic surgery of a patient with Hypohidrotic ectodermal dysplasia with cleft palate: A Clinical report

  • 김좌영 (한림대학교강남성심병원 구강악안면외과) ;
  • 박인영 (한림대학교성심병원 교정과) ;
  • 송윤정 (관악서울대학교치과병원 보존과)
  • Kim, Jwa-Young (Department of Oral and Maxillofacial Surgery, Hallym University Kangnam Sacred Heart Hospital) ;
  • Park, In-Young (Department of Orthodontics, Hallym University Sacred Heart Hospital) ;
  • Song, Yun-Jung (Department of Conservative Dentistry, Seoul National University Gwanak Dental Hospital)
  • 발행 : 2019.01.31
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초록

Ectodermal dysplasia is a genetic disorder in which various clinical manifestations involve two or more of the differentiated tissues of the ectoderm. Facial deformity, which is frequently associated with ectodermal dysplasia, appears in the form of cleft lip or cleft palate, especially in the middle facial area.Cleft and tooth defects result in decreased alveolar bone development.This leads to severe skeletal incongruity. Facial features include frontal protrusion, malar bone hypoplasia, flat nose, mandibular prominence and long lower facial height. This clinical report presents treatment including orthognathic surgery of a patient with Hypohidrotic Ectodermal dysplasia with cleft palate.

키워드

참고문헌

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