• Journal of Korean Neurosurgical Society
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• 제67권3호
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• pp.270-279
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• 2024

Prompt medical attention is crucial for congenital intracranial vascular malformations in children and newborns due to potential severe outcomes. Imaging is pivotal for accurate identification, given the diverse risks and treatment strategies. This article aims to enhance the identification and understanding of congenital intracranial vascular abnormalities including arteriovenous malformation, arteriovenous fistula, cavernous malformation, capillary telangiectasia, developmental venous anomaly, and sinus pericranii in pediatric patients.

• 대한골관절종양학회지
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• 제14권1호
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• pp.56-61
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• 2008

보고된 반 이상의 선천성 동정맥 기형이 사지에 발생한다. 그러나 주로 연부 조직에 발생하며 골 내에 생기는 경우는 적어 이에 대한 연구가 드물다. 또한 복잡하고 다양한 임상양상 때문에 진단 및 치료가 어려운 것으로 알려져 있다. 20개월 된 소아 여자 환자가 좌측 하지의 외상 없이 발생한 박동성 종괴를 주소로 내원하였다. 저자들은 경골 내에 발생한 동정맥 기형을 경험하고 에탄올 주입을 이용한 색전술로 좋은 결과를 얻었기에 문헌고찰과 함께 보고하는 바이다.

• Journal of Korean Neurosurgical Society
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• 제67권3호
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• pp.315-325
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• 2024

Vascular malformations are structural abnormalities that are thought to result from errors in vasculogenesis and angiogenesis during embryogenesis. Vascular malformations of the scalp present unique management challenges due to aesthetic and functional implications. This review examines the pathophysiology, clinical presentation, and management techniques for six common types of vascular malformations of the face and scalp : infantile hemangioma, capillary malformations, venous malformations, lymphatic malformations, arteriovenous malformations, and arteriovenous fistulas. These lesions range from common to rare, and have very different natural histories and management paradigms. There has been increasing understanding of the molecular pathways that are altered in association with these vascular lesions and these molecular targets may represent novel strategies of treating lesions that have historically been approached from a structural perspective only.

• Journal of Korean Neurosurgical Society
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• 제67권3호
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• pp.326-332
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• 2024

Intracranial vascular malformations typically encountered by pediatric neurosurgeons include arteriovenous malformations, vein of Galen malformations and cavernous malformations. While these remain amongst some of the most challenging lesions faced by patients and caregivers, the past decade has produced marked advances in the understanding of the pathophysiology of these conditions, with concomitant innovations in treatment. This article will highlight present and future perspectives relevant to these diseases, with a focus on an emerging approach utilizing disease-specific mutations to develop a novel taxonomy for these conditions.

• Journal of Korean Neurosurgical Society
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• 제67권3호
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• pp.289-298
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• 2024

Pediatric intracranial arteriovenous malformations (AVMs) are challenging lesions managed by pediatric neurosurgeons. The high risk of hemorrhage and neurologic injury is compounded by the unique anatomy of each malformation that requires individualizing treatment options. This article reviews the current status of pediatric AVM epidemiology, pathophysiology and clinical care, with a specific focus on the rationale and methodology of surgical resection.

• Journal of Korean Neurosurgical Society
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• 제67권3호
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• pp.280-288
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• 2024

Brain arteriovenous malformations (bAVMs) are aberrant arteriovenous shunts through a vascular nidus with no intervening capillary beds. They are one of the commonest causes of spontaneous intracranial haemorrhage in children and may be associated with significant morbidity and mortality in cases of rupture. Treatment strategies include microsurgical resection, endovascular embolisation, stereotactic radiosurgery, multimodality treatment with a combination thereof, and particularly in high-grade bAVMs, conservative management. Clinicians involved in treating bAVMs need to have familiarity with the natural history pertaining to bAVMs in terms of risk of rupture, risk factors elevating rupture risk as well as understanding the clinical manifestations of bAVMs. This invited review serves to provide a synthesis on natural history and clinical presentation of bAVMs with particular focus in children to inform decision-making pertaining to management.

• Journal of Chest Surgery
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• 제29권7호
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• pp.802-806
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• 1996

Arteriovenous malformations are vascular anomalies containing a communication between artery and vein without an intervening capillary bed and also are the most dangerous of vascular malformations being hemodynamically active. Treatment must be careful usually limited and considered in the phase of activity of hemodynamics. The patient was 29-year-old female and had no specific signs and symptoms except buldging, pal- pable mass on the right posterolateral chest wall from several years ago and it was gradually growing from that time. The operation was done with ligation of the right 9th, 1 Oth intercostal arteries and dissection from other normal tissues and then excised the arteriovenous malformation mass and its feeding vessels. The pathologic result was arteriovenous malformation.

• Imaging Science in Dentistry
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• 제41권3호
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• pp.123-128
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• 2011

Arteriovenous malformations are extremely rare conditions in that can result from abnormalities in the structure of blood vessels, which may be potentially fatal. A 30-year-old female patient visited our hospital with a complaint of swelling on the right maxillary posterior gingiva along with the large port-wine stain on right side of face. On clinical examination, the swelling was compressible and pulsatile. Radiographic examination revealed a lytic lesion of maxilla. Diagnostic angiography revealed a high-flow arteriovenous malformation of maxilla which was treated by selective transarterial embolization of maxillary artery using polyvinyl alcohol particles.

• Archives of Plastic Surgery
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• 제34권3호
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• pp.399-402
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• 2007

Purpose: Arteriovenous fistula is one of high flow vascular malformations. Recently, arteriovenous fistula has been regarded as one of the type of arteriovenous malformations. The patients were diagnosed as arteriovenous malformation Schobinger clinical stage II. Even though arteriovenous fistula rarely occurs on head and neck, treatment of that is difficult due to frequent recurrence. In treating the arteriovenous fistula, chemical embolization, surgical excision and other treatment modalities were used, but the results were not satisfactory. The authors experienced three cases of arteriovenous fistula and treated them with surgical excision. Methods: In cases, warmth, enlargement, pulsation, thrill, and bruit were found. For the accurate evaluation before the operation, angiography and MRI were checked in advance. Incision was made on the site of pulsation. The artery and vein connected to the arteriovenous fistula were dissected widely, individually ligated, and divided. And then the entire mass was totally removed. Results: All surgical sites were healed well without complications and there was no evidence of recurrence in all cases up to for 2 years of follow-up examination. Conclusion: The arteriovenous fistula on face is a very rare disease and has difficulties in treatment. The authors experienced three cases of arteriovenous fistula with complete surgical removal and no recurrence was found in all cases.

• 대한소아치과학회지
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• 제49권2호
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• pp.228-233
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• 2022

동정맥 기형(Arteriovenous malformations, AVMs)은 동맥과 정맥이 직접적으로 연결되어 모세혈관과 연결되지 않은 희귀한 선천성 기형 중 하나이다. AVM은 유아기 후반이나 소아기까지는 임상적으로 나타나지 않을 수 있다. 특히 안면 AVM은 생명을 위협하는 치과적 응급 상황을 일으킬 수 있다. 전신병력이 없는 만 5세 여아가 하악 좌측 제2유구치의 후방 치은 주위의 자발적인 잇몸 출혈로 내원하였다. 감별진단 및 치료를 위해 전신마취 하에 대퇴정맥 접근을 통한 혈관조영술이 시행되었다. 동맥색전술 만으로도 혈류량이 효과적으로 감소되었다. 5개월 동안의 경과관찰에서 재발되지 않았다. 본 연구는 성장기 환자에서 이환된 혈관의 색전술이 외과적 절제술보다 더 효과적이고 안전한 방법이 될 수 있다고 보고하는 바이다.