Polyostotic Fibrous Dysplasia of Cranio-Maxillofacial Area

두개 악안면 부위에 발생한 다골성 섬유성이형성증

  • Han Jin-Woo (Department of Oral and Maxillofacial Radiology, College of Dentistry, Kangnung National University) ;
  • Kwon Hyuk-Rok (Department of Oral and Maxillofacial Radiology, College of Dentistry, Kangnung National University) ;
  • Lee Jin-Ho (Department of Oral and Maxillofacial Radiology, College of Dentistry, Kangnung National University) ;
  • Park In-Woo (Department of Oral and Maxillofacial Radiology, College of Dentistry, Kangnung National University)
  • 한진우 (강릉대학교 치과대학 구강악안면방사선학교실) ;
  • 권혁록 (강릉대학교 치과대학 구강악안면방사선학교실) ;
  • 이진호 (강릉대학교 치과대학 구강악안면방사선학교실) ;
  • 박인우 (강릉대학교 치과대학 구강악안면방사선학교실)
  • Published : 2000.06.01

Abstract

Fibrous dysplasia is believed to be a hamartomatous developmental lesion of unknown origin. This disease is divided into monostotic and polyostotic fibrous dysplasia. Polyostotic type can be divided into craniofacial type, Lichtenstein-Jaffe type, and McCune-Albright syndrome. In this case, a 31-year-old female presented spontaneous loss of right mandibular teeth before 5 years and has shown continuous expansion of right mandibular alveolus. Through the radiographic view, the coarse pattern of the mixed radiopaque-lucent lesion was seen on the right mandibular body, and there was diffuse pattern of the mixed radiopaque-lucent lesion with ill-defined margin in the left mandibular body. In the right calvarium, the lesion had cotton-wool appearance. Partial excision for contouring, multiple extraction, and alveoloplasty were accomplished under general anesthesia for supportive treatment. Finally we could conclude this case was polyostotic fibrous dysplasia of cranio-maxillofacial area based on the clinical, radiologic finding, and histopathologic examination.

Keywords