Clinical and Experimental Pediatrics

대한소아청소년과학회 (The Korean Pediatric Society)
권호 표지

선천성 심장질환을 가진 영아에서 발견된 폐 격리증을 동반하지 않은 폐의 이상 체 동맥 기시 1례

Anomalous systemic arterial supply to lung without sequestration in an infant who has congenital heart disease : a case report

  • 장연우 (가천의과대학교 길병원 심장센터 소아심장과) ;
  • 최덕영 (가천의과대학교 길병원 심장센터 소아심장과)
  • Jang, Yeon Woo (Division of Pediatric Cardiology, Heart Center, Gil Medical Center, Gachon Medical School) ;
  • Choi, Duck Young (Division of Pediatric Cardiology, Heart Center, Gil Medical Center, Gachon Medical School)
  • 투고 : 2006.04.03
  • 심사 : 2006.05.11
  • 발행 : 2006.08.15
PDF 다운로드
⟨ 이전 논문 다음 논문 ⟩

초록

폐 격리증이 없는 정상적인 폐에 체 혈관이 이상 기시하는 것은 매우 드문 질환이다. 저자들은 반복적인 하기도 감염을 보이는 영아에서 선천성 심장질환의 상태가 본 하기도 감염을 나타낼 정도로 심하지 않음을 이상히 여겨 컴퓨터 단층 촬영을 시행하였다. 그 결과 폐 격리증이 없는 폐의 이상 체 동맥 기시가 우측 폐하 엽에 존재함과 동시에 우측 하엽 폐동맥이 없는 사실을 확인하게 되었다. 어린 나이에 이 같은 선천성 질환의 조합은 이전에 보고 된 바가 없는 매우 드문 질환으로 생각된다.

Systemic arterial supply from the aorta to the lung is a rare congenital anomaly within the spectrum of bronchopulmonary sequestration according to Pryce's terminology. We describe our experience of this anomaly in an infant with congenital cardiac disease confirmed by multidetector CT scan. We found a systemic arterial supply from the aorta to the right lower lobe of lung without right lower lobar pulmonary artery and bronchopulmonary sequestration. This combination of congenital anomaly is most rare form.

키워드

참고문헌

  1. Felker RE, Tonkin ILD. Imaging of pulmonary sequestration. Am J Roentgenol 1990;154:241-9 https://doi.org/10.2214/ajr.154.2.2105007
  2. Painter RL, Billig DM, Epstein I. Anomalous systemic arterialization of the lung without sequestration. N Engl J Med 1968;279:866-7 https://doi.org/10.1056/NEJM196810172791606
  3. Kirks DR, Kane PE, Free EA, Taybi H. Systemic arterial supply to normal basilar segments of the left lower lobe. Am J Roentgenol 1976;126:817-21 https://doi.org/10.2214/ajr.126.4.817
  4. Pryce DM, Sellors TH, Blair LG. Intralobar sequestration of lung associated with an abnormal pulmonary artery. Br J Surg 1947;35:18-29 https://doi.org/10.1002/bjs.18003513704
  5. Pryce DM. Lower accessory pulmonary with intralobar sequestration of lung:report of seven cases. J Pathol 1946; 58:457-67 https://doi.org/10.1002/path.1700580316
  6. Iizasa T, Haga Y, Hiroshima K, Fujisawa T. Systemic arterial supply to the basal segment without the pulmonary artery : four consecutive cases. Eur J Car Thorc Surg 2003; 23:847-9 https://doi.org/10.1016/S1010-7940(03)00087-3
  7. Yamanaka A, Hirai T, Fujimoto T, Hase M, Noguchi M, Konishi F. Anomalous systemic arterial supply to normal basal segments of the left lower lobe. Ann Thorac Surg 1999;68:332-8 https://doi.org/10.1016/S0003-4975(99)00533-0
  8. Ellis K. Developmental abnormalities in the systemic blood supply to the lungs. Am J Roentgenol 1991;156:669-79 https://doi.org/10.2214/ajr.156.4.2003427
  9. Kurosaki Y, Kurosaki A, Irimoto M, Kuramoto K, Itai Y. Systemic arterial supply to normal basal segments of left lower lobe : CT findings. J Comput Assist Tomogr 1993; 17:857-61 https://doi.org/10.1097/00004728-199311000-00004
  10. Miyake H, Hori Y, Takeoka H, Takuma M, Kawagoe T, Mori H. Systemic arterial supply to normal basal segments of the left lung : characteristic features on chest radiography and CT. Am J Roentgenol 1998;171:387-92 https://doi.org/10.2214/ajr.171.2.9694458
  11. Livingston DR, Hehta AC, O'Donoval PB, Cordasco EM. An angiographic dilemma : bronchopulmonary sequestration vs pseudosequestration : case reports. Angiology 1986;37: 896-904
  12. Stein PD, Beemath A, Kayali F, Skaf E, Sanchez J, Olson RE. Multidetector computed tomography for the diagnosis of coronary artery disease : a systemic review. Am J Med 2006;119:203-16 https://doi.org/10.1016/j.amjmed.2005.06.071