Clinical and Experimental Pediatrics

대한소아청소년과학회 (The Korean Pediatric Society)
권호 표지

단백 소실성 장병증을 동반한 교착성 심낭염 1례

A case of constrictive pericarditis presenting with protein-losing enteropathy

  • 홍정미 (경희대학교 의과대학 소아과학교실) ;
  • 이재영 (부천세종병원 소아과) ;
  • 김수진 (부천세종병원 소아과) ;
  • 장기영 (부천세종병원 소아과) ;
  • 심우섭 (부천세종병원 소아과)
  • Hong, Jeong Mi (Department of Pediatrics, College of Medicine, Kyunghee University) ;
  • Lee, Jae Young (Department of Pediatric Cardiology, Sejong Heart Institute, Sejong General Hospital) ;
  • Kim, Soo Jin (Department of Pediatric Cardiology, Sejong Heart Institute, Sejong General Hospital) ;
  • Jang, Gi Young (Department of Pediatric Cardiology, Sejong Heart Institute, Sejong General Hospital) ;
  • Shim, Woo Sup (Department of Pediatric Cardiology, Sejong Heart Institute, Sejong General Hospital)
  • 투고 : 2006.02.24
  • 심사 : 2006.05.12
  • 발행 : 2006.08.15
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초록

소아에서 교착성 심낭염은 매우 드문 질환으로 이에 의하여 단백 소실성 장병증이 동반되는 경우는 더욱 드물다. 저자들은 교착성 심낭염의 주요 증상의 하나로 단백 소실성 장병증을 보인 여아 1례를 경험하였기에 문헌고찰과 함께 보고하는 바이다.

Constrictive pericarditis represents a rare cause of protein-losing enteropathy in children. Reported is an 11-year-old girl with protein-losing enteropathy (PLE) as the principal manifestations of constrictive pericarditis. After total pericardiectomy, symptoms and signs of PLE disappeared. Doppler echocardiography including tissue Doppler imaging is a useful noninvasive initial diagnostic tool for differential diagnosis of diastolic heart failure.

키워드

참고문헌

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