Tuberculosis and Respiratory Diseases

The Korean Academy of Tuberculosis and Respiratory Diseases (대한결핵및호흡기학회)
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Lymphoid Interstitial Pneumonia Associated with Primary Sjogren's Syndrome - A Case Report

일차성 Sjogren씨 증후군에서 발생한 림프구성 간질성 폐렴 1예: 증례보고와 국내문헌고찰

  • Mo, Sang-Il (Department of Internal Medicine, Soonchunhyang University College of Medicine) ;
  • Lee, Hyeok-Gyu (Department of Internal Medicine, Soonchunhyang University College of Medicine) ;
  • Cho, A-Ra (Department of Internal Medicine, Soonchunhyang University College of Medicine) ;
  • Chung, Hye-Kyoung (Department of Internal Medicine, Soonchunhyang University College of Medicine) ;
  • Lee, Ho-Sung (Department of Internal Medicine, Soonchunhyang University College of Medicine) ;
  • Choi, Jae-Sung (Department of Internal Medicine, Soonchunhyang University College of Medicine) ;
  • Seo, Ki-Hyun (Department of Internal Medicine, Soonchunhyang University College of Medicine) ;
  • Nah, Seong-Su (Department of Internal Medicine, Soonchunhyang University College of Medicine) ;
  • Kim, Yong-Hoon (Department of Internal Medicine, Soonchunhyang University College of Medicine) ;
  • Na, Ju-Ock (Department of Internal Medicine, Soonchunhyang University College of Medicine)
  • 모상일 (순천향대학교 의과대학 내과학교실) ;
  • 이혁규 (순천향대학교 의과대학 내과학교실) ;
  • 조아라 (순천향대학교 의과대학 내과학교실) ;
  • 정혜경 (순천향대학교 의과대학 내과학교실) ;
  • 이호성 (순천향대학교 의과대학 내과학교실) ;
  • 최재성 (순천향대학교 의과대학 내과학교실) ;
  • 서기현 (순천향대학교 의과대학 내과학교실) ;
  • 나성수 (순천향대학교 의과대학 내과학교실) ;
  • 김용훈 (순천향대학교 의과대학 내과학교실) ;
  • 나주옥 (순천향대학교 의과대학 내과학교실)
  • Received : 2010.09.09
  • Accepted : 2010.11.05
  • Published : 2010.11.30
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Abstract

Lymphoid interstitial pneumonia (LIP) is a rare benign lymphoproliferative interstitial lung disease. LIP has been associated with autoimmune disorders, HIV, viral infections, and so on. Once underlying systemic diseases have been excluded, a diagnosis of idiopathic LIP can be made. Although 6 cases of pathologically confirmed LIP have occurred in Korea, thus far none has been associated with primary Sjogren's syndrome. A 44-year-old man was admitted to hospital due to a dry cough and dypsnea on exertion that had been ongoing for 2 months. A chest radiography showed multiple and variable-sized cystic lesions, on both lungs and both interstitial infiltration and consolidation in both lower lung fields. Tests for autoantibody showed positive results of anti-nuclear antibody and anti-Ro/La antibody. The patient underwent a video assisted thoracoscopic surgery biopsy and pathologically confirmed LIP. We report the first known case of LIP-associated with primary Sjogren's syndrome in Korea.

Keywords

References

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