Journal of Yeungnam Medical Science

Yeungnam University College of Medicine, Yeungnam University Institute Medical Science (영남대 의대 학술지 편집위원회)
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Lymphocytic interstitial pneumonia in a patient with Sjögren's syndrome

  • Lee, Eun Hye (Division of Pulmonology, Department of Internal Medicine, Yonsei University College of Medicine) ;
  • Park, Ji Eun (Division of Pulmonology, Department of Internal Medicine, Yonsei University College of Medicine) ;
  • Goag, Eun Kyong (Division of Pulmonology, Department of Internal Medicine, Yonsei University College of Medicine) ;
  • Kim, Young Joo (Division of Pulmonology, Department of Internal Medicine, Yonsei University College of Medicine) ;
  • Jung, In Young (Division of Pulmonology, Department of Internal Medicine, Yonsei University College of Medicine) ;
  • Kim, Chi Young (Division of Pulmonology, Department of Internal Medicine, Yonsei University College of Medicine) ;
  • Park, Young Mok (Division of Pulmonology, Department of Internal Medicine, Yonsei University College of Medicine) ;
  • Lee, Jung Mo (Division of Pulmonology, Department of Internal Medicine, Yonsei University College of Medicine) ;
  • Park, Moo Suk (Division of Pulmonology, Department of Internal Medicine, Yonsei University College of Medicine)
  • Received : 2015.04.02
  • Accepted : 2015.05.19
  • Published : 2016.11.18
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Abstract

Lymphocytic interstitial pneumonia (LIP) is a rare benign lymphoproliferative disorder characterized by diffuse infiltration of the pulmonary parenchymal interstitium by polyclonal lymphocytes and plasma cells. LIP has been associated with a variety of clinical conditions; such as connective tissue disorders and other immune system abnormalities. Treatment usually involves administration of corticosteroids and other immunosuppressants. We report on a 38-year-old female patient who complained of shortness of breath, dry mouth, and dry eyes for more than 1 month, and was positive for Raynaud's phenomenon. Based on surgical biopsy, she was diagnosed as having LIP accompanied by $Sj{\ddot{o}}gren^{\prime}s$ syndrome. The patient was treated with high-dose steroids followed by maintenance therapy for approximately 2 years, and her condition improved.

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References

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