Journal of Yeungnam Medical Science

Yeungnam University College of Medicine, Yeungnam University Institute Medical Science (영남대 의대 학술지 편집위원회)
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Dermatomyositis sine dermatitis, a rare phenotype of idiopathic inflammatory myopathy

  • Park, Jin-Sung (Department of Neurology, Kyungpook National University School of Medicine) ;
  • Park, Ji-Young (Department of Pathology, Kyungpook National University School of Medicine)
  • Received : 2017.04.26
  • Accepted : 2017.05.25
  • Published : 2017.06.30
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Abstract

Dermatomyositis (DM) is characterized by progressive proximal limb weakness and typical skin manifestations. The histological findings that show perifascicular atrophy and deposition of membrane attack complex are pathognomic features of DM. Dermatomyositis is categorized into classical DM and non-classical DM, which includes amyopathic DM and DM sine dermatitis. DM sine dermatitis is seldom described because of its rarity, making the diagnosis more challenging. We report a case of DM sine dermatitis, a rare phenotype of DM.

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References

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  1. Anti-MDA5 Antibody-Positive Interstitial Pneumonia with Autoimmune Features Presenting as Amyopathic Hypodermatitic Dermatomyositis: A Case Report vol.13, pp.1, 2017, https://doi.org/10.1159/000515245